A Case of Juvenile Dermatomyositis .

Yom,  Hye Won; Park,  Ji Hye; Seo,  Jeong Wan; Choi,  Hye Young; Gu,  Hesoo; Lee,  Sun Wha; Kang,  Yun Jong

Case Report

Journal of the Korean Child Neurology Society 2003;11(1):178-183.
Published online May 30, 2003.

A Case of Juvenile Dermatomyositis .

Hye Won Yom, Ji Hye Park, Jeong Wan Seo, Hye Young Choi, Hesoo Gu, Sun Wha Lee, Yun Jong Kang

¹Department of Pediatrics, College of Medicine, Ewha Woman's University, Seoul, Korea. jwseo@ewha.ac.kr
²Department of Dermatology, College of Medicine, Ewha Woman's University, Seoul, Korea.
³Department of Pathology, College of Medicine, Ewha Woman's University, Seoul, Korea.
⁴Department of Radiology, College of Medicine, Ewha Woman's University, Seoul, Korea.
⁵Department of Pediatrics, Halla Hospital, Jeju, Korea.

Abstract

Juvenile dermatomyositis is an uncommon autoimmune disease with classic heliotrope discoloration of eyelids, erythematous skin rash of joints and proximal muscle weakness. Quite different from adults, malignancy is rarely accompanied in juvenile dermatomyositis. However vasculitis, muscle atrophy, calcification and gastrointestinal involvement are often observed in juvenile dermatomyositis. A six year old boy was admitted with chief complaints of general weakness and skin rash. Muscle biopsy was performed which was consistent with dermatomyositis. The patient was treated with intravenous immunoglobulin, steroid, methotrexate and physiotherapy. We report a case of juvenile dermatomyositis.

Key Words: Juvenile dermatomyositis