A Case of Chiari III Malformation.

Cho,  Eun Young; Lee,  Jong Joo; Lim,  Jae Woo; Choen,  Eun Jung; Ko,  Kyoung Og; Lee,  Young Hyuk

Case Report

Journal of the Korean Child Neurology Society 2005;13(2):282-287.
Published online November 30, 2005.

A Case of Chiari III Malformation.

Eun Young Cho, Jong Joo Lee, Jae Woo Lim, Eun Jung Choen, Kyoung Og Ko, Young Hyuk Lee

¹Department of Pediatrics, College of Medicine, Konyang University, Daejeon, Korea. y2hyuk@unitel.co.kr
²Department of Neurosurgery, College of Medicine, Konyang University, Daejeon, Korea.

Abstract

Chiari malformations are brain stem anomalies with or without spinal canal involvement. Type III is the rarest of the Chiari malformations and is characterized by a low occipital or high cervical encephalocele in combination with multiple cerebellar and brain stem anomalies. We report a case of Chiari III malformation of a newborn, who underwent repair of occipital meningoencephalocele and endoscopic third ventriculostomy. We present the case with a review of related literature.

Key Words: Chiari III malformation